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dc.contributor.authorKaraca, Meryem
dc.date.accessioned2021-03-02T20:51:27Z
dc.date.available2021-03-02T20:51:27Z
dc.identifier.citationKaraca M., "Evaluation of Echocardiographic Findings of Mucopolysaccharidosis Cases", European Archives of Medical Research, cilt.35, ss.167-169, 2019
dc.identifier.issn2651-3137
dc.identifier.otherav_040bf5e0-cc62-4664-968c-36dc8b170bad
dc.identifier.othervv_1032021
dc.identifier.urihttp://hdl.handle.net/20.500.12627/8658
dc.identifier.urihttps://doi.org/10.4274/eamr.galenos.2019.92486
dc.identifier.urihttps://avesis.istanbul.edu.tr/api/publication/040bf5e0-cc62-4664-968c-36dc8b170bad/file
dc.description.abstractObjective: Mucopolysaccharidosis (MPS) is a lysosomal storage disease in which the degradation of glycosaminoglycans is impaired. Cardiac involvement may occur in different ways in all types of the disease. In this study, we aimed to evaluate the echocardiographic reports of our patients with MPS retrospectively. Methods: Echocardiography reports of 37 patients with MPS were reviewed retrospectively. Results: Cardiac involvement was present in 70.2% our patients and the most commonly involved structure was mitral valve (59.5%). The most common pathology in mitral valve was mitral valve regurgitation (51.4%). Conclusion: Cardiac involvement and complications are frequently seen in MPS. Heart failure, coronary artery involvement and arrhythmias are the main causes of death. Early diagnosis of MPS and early initiation of enzyme replacement therapy may improve cardiac involvement. Progressive valve involvement may require surgical intervention over time. For all these reasons, cardiac evaluation in MPS patients should be performed at least once a year with accompanying electrocardiogram and echocardiography.
dc.language.isotur
dc.subjectKlinik Tıp (MED)
dc.subjectSağlık Bilimleri
dc.titleEvaluation of Echocardiographic Findings of Mucopolysaccharidosis Cases
dc.typeMakale
dc.relation.journalEuropean Archives of Medical Research
dc.contributor.departmentİstanbul Üniversitesi , İstanbul Tıp Fakültesi , Dahili Tıp Bilimleri Bölümü
dc.identifier.volume35
dc.identifier.startpage167
dc.identifier.endpage169
dc.contributor.firstauthorID1222143


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