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dc.contributor.authorGoksel, Onur S.
dc.contributor.authorTireli, Emin
dc.contributor.authorDayioglu, Enver
dc.contributor.authorEl, Helin
dc.date.accessioned2021-03-04T11:18:43Z
dc.date.available2021-03-04T11:18:43Z
dc.date.issued2009
dc.identifier.citationGoksel O. S. , El H., Tireli E., Dayioglu E., "Combined Aortic and Mitral Valve Replacement in a Child with Mucopolysaccharidosis Type I: A Case Report", JOURNAL OF HEART VALVE DISEASE, cilt.18, sa.2, ss.214-216, 2009
dc.identifier.issn0966-8519
dc.identifier.othervv_1032021
dc.identifier.otherav_71b50c9f-0b7f-4db7-8de8-c1f68324cc99
dc.identifier.urihttp://hdl.handle.net/20.500.12627/78290
dc.description.abstractMucopolysaccaridosis syndromes are metabolic disorders that are inherited in an autosomal recessive pattern, and demonstrate cardiovascular involvement that, on rare occasions, results in surgery. The case is presented of a 12-year-old boy with symptoms and signs of congestive heart failure who was referred to the authors' department for severe mitral and aortic valvular stenosis. The patient was shown to have the somatic characteristics of mucopolysaccharidosis, while urinalysis indicated the presence of chondroitin sulfate B. Mitral and aortic valve replacements were carried out, using bileaflet mechanical valves with a standard median sternotomy and cardiopulmonary bypass. A bileaflet preservation technique was adopted during mitral valve replacement to provide better hemodynamics. Severe cardiac involvement in mucopolysaccharidosis requiring cardiac surgery in pediatrics has been rarely documented. A low-profile bileaflet mechanical valve, enabling a larger-sized valve insertion, is preferred in order to avoid patient-prosthesis mismatch during somatic growth of the patient.
dc.language.isoeng
dc.subjectTıp
dc.subjectKardiyoloji
dc.subjectSağlık Bilimleri
dc.subjectDahili Tıp Bilimleri
dc.subjectKlinik Tıp (MED)
dc.subjectKlinik Tıp
dc.subjectCARDIAC ve CARDIOVASCULAR SİSTEMLER
dc.titleCombined Aortic and Mitral Valve Replacement in a Child with Mucopolysaccharidosis Type I: A Case Report
dc.typeMakale
dc.relation.journalJOURNAL OF HEART VALVE DISEASE
dc.contributor.departmentİstanbul Üniversitesi , ,
dc.identifier.volume18
dc.identifier.issue2
dc.identifier.startpage214
dc.identifier.endpage216
dc.contributor.firstauthorID191317


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